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The Aggregation-Prone Intracellular Serpin SRP-2 Fails to Transit the ER in Caenorhabditis elegans

Familial encephalopathy with neuroserpin inclusions bodies (FENIB) is a serpinopathy that induces a rare form of presenile dementia. Neuroserpin contains a classical signal peptide and like all extracellular serine proteinase inhibitors (serpins) is secreted via the endoplasmic reticulum (ER)–Golgi...

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書目詳細資料
發表在:Genetics
Main Authors: Silverman, Richard M., Cummings, Erin E., O’Reilly, Linda P., Miedel, Mark T., Silverman, Gary A., Luke, Cliff J., Perlmutter, David H., Pak, Stephen C.
格式: Artigo
語言:Inglês
出版: Genetics Society of America 2015
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在線閱讀:https://ncbi.nlm.nih.gov/pmc/articles/PMC4423363/
https://ncbi.nlm.nih.gov/pubmed/25786854
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1534/genetics.115.176180
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