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Converging mechanisms in ALS and FTD: Disrupted RNA and protein homeostasis

Breakthrough discoveries identifying common genetic causes for amyotrophic lateral sclerosis (ALS) and frontotemporal dementia (FTD) have transformed our view of these disorders. They share unexpectedly similar signatures, including dysregulation in common molecular players including TDP-43, FUS/TLS...

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Detalles Bibliográficos
Publicado en:Neuron
Main Authors: Ling, Shuo-Chien, Polymenidou, Magdalini, Cleveland, Don W.
Formato: Artigo
Idioma:Inglês
Publicado: 2013
Assuntos:
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC4411085/
https://ncbi.nlm.nih.gov/pubmed/23931993
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.neuron.2013.07.033
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