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A role for destabilizing amino acid replacements in light-chain amyloidosis.

Light-chain (L-chain) amyloidosis is characterized by deposition of fibrillar aggregates composed of the N-terminal L-chain variable region (VL) domain of an immunoglobulin, generally in individuals overproducing a monoclonal L chain. In addition to proteolytic fragmentation and high protein concent...

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Detalhes bibliográficos
Main Authors: Hurle, M R, Helms, L R, Li, L, Chan, W, Wetzel, R
Formato: Artigo
Idioma:Inglês
Publicado em: 1994
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC44012/
https://ncbi.nlm.nih.gov/pubmed/8202506
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