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Regulation of Sterol Transport between Membranes and NPC2()

Niemann-Pick disease type C (NPC) is caused by defects in either the NPC1 or NPC2 gene and is characterized by accumulation of cholesterol and glycolipids in the late endosome/lysosome compartment. NPC2 is an intralysosomal protein that binds cholesterol in vitro. Previous studies demonstrated rapid...

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Dettagli Bibliografici
Pubblicato in:Biochemistry
Autori principali: Xu, Zhi, Farver, William, Kodukula, Sarala, Storch, Judith
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2008
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4355403/
https://ncbi.nlm.nih.gov/pubmed/18823126
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1021/bi801328u
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