Načítá se...

Brain white matter volume abnormalities in Lesch-Nyhan disease and its variants

OBJECTIVE: We sought to examine brain white matter abnormalities based on MRI in adults with Lesch-Nyhan disease (LND) or an attenuated variant (LNV) of this rare, X-linked neurodevelopmental disorder of purine metabolism. METHODS: In this observational study, we compared 21 adults with LND, 17 with...

Celý popis

Uloženo v:
Podrobná bibliografie
Vydáno v:Neurology
Hlavní autoři: Schretlen, David J., Varvaris, Mark, Vannorsdall, Tracy D., Gordon, Barry, Harris, James C., Jinnah, H.A.
Médium: Artigo
Jazyk:Inglês
Vydáno: Lippincott Williams & Wilkins 2015
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC4336080/
https://ncbi.nlm.nih.gov/pubmed/25503620
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1212/WNL.0000000000001128
Tagy: Přidat tag
Žádné tagy, Buďte první, kdo otaguje tento záznam!