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Sodium channel slow inactivation as a therapeutic target for myotonia congenita

OBJECTIVE: Patients with myotonia congenita have muscle hyperexcitability due to loss-of-function mutations in the chloride channel in skeletal muscle, which causes spontaneous firing of muscle action potentials (myotonia), producing muscle stiffness. In patients, muscle stiffness lessens with exerc...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:Ann Neurol
Egile Nagusiak: Novak, Kevin R, Norman, Jennifer, Mitchell, Jacob R, Pinter, Martin J, Rich, Mark M
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: 2015
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC4315705/
https://ncbi.nlm.nih.gov/pubmed/25515836
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/ana.24331
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