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TDP-43 Toxicity Proceeds via Calcium Dysregulation and Necrosis in Aging Caenorhabditis elegans Motor Neurons

Amyotrophic lateral sclerosis (ALS) is a heterogeneous disease with either sporadic or genetic origins characterized by the progressive degeneration of motor neurons. At the cellular level, ALS neurons show protein misfolding and aggregation phenotypes. Transactive response DNA-binding protein 43 (T...

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Détails bibliographiques
Publié dans:J Neurosci
Auteurs principaux: Aggad, Dina, Vérièpe, Julie, Tauffenberger, Arnaud, Parker, J. Alex
Format: Artigo
Langue:Inglês
Publié: Society for Neuroscience 2014
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Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC4262699/
https://ncbi.nlm.nih.gov/pubmed/25186754
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1523/JNEUROSCI.2495-13.2014
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