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Tubulin hyperacetylation is adaptive in cardiac proteotoxicity by promoting autophagy

Proteinopathy causes cardiac disease, remodeling, and heart failure but the pathological mechanisms remain obscure. Mutated αB-crystallin (CryAB(R120G)), when expressed only in cardiomyocytes in transgenic (TG) mice, causes desmin-related cardiomyopathy, a protein conformational disorder. The diseas...

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Publicado en:Proc Natl Acad Sci U S A
Autores principales: McLendon, Patrick M., Ferguson, Bradley S., Osinska, Hanna, Bhuiyan, Md. Shenuarin, James, Jeanne, McKinsey, Timothy A., Robbins, Jeffrey
Formato: Artigo
Lenguaje:Inglês
Publicado: National Academy of Sciences 2014
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4260547/
https://ncbi.nlm.nih.gov/pubmed/25404307
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1415589111
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