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Von Willebrand's disease with spontaneous platelet aggregation induced by an abnormal plasma von Willebrand factor.

We have investigated and characterized the abnormalities in four unrelated patients with von Willebrand's disease (vWd) who have (a) enhanced ristocetin-induced platelet aggregation (RIPA) at low ristocetin concentrations, (b) absence of the largest plasma von Willebrand factor (vWf) multimers, and...

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Detalles Bibliográficos
Publicado en:J Clin Invest
Autores principales: Grainick, H R, Williams, S B, McKeown, L P, Rick, M E, Maisonneuve, P, Jenneau, C, Sultan, Y
Formato: Artigo
Lenguaje:Inglês
Publicado: American Society for Clinical Investigation 1985
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Acceso en línea:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC424119/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/2932469/
https://ncbi.nlm.nih.govhttps://doi.org/10.1172/JCI112132
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