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Von Willebrand's disease with spontaneous platelet aggregation induced by an abnormal plasma von Willebrand factor.

We have investigated and characterized the abnormalities in four unrelated patients with von Willebrand's disease (vWd) who have (a) enhanced ristocetin-induced platelet aggregation (RIPA) at low ristocetin concentrations, (b) absence of the largest plasma von Willebrand factor (vWf) multimers,...

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Autors principals: Grainick, H R, Williams, S B, McKeown, L P, Rick, M E, Maisonneuve, P, Jenneau, C, Sultan, Y
Format: Artigo
Idioma:Inglês
Publicat: 1985
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC424119/
https://ncbi.nlm.nih.gov/pubmed/2932469
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