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Development of microscopic polyangiitis-related pulmonary fibrosis in a patient with autoimmune pulmonary alveolar proteinosis

BACKGROUND: Autoimmune pulmonary alveolar proteinosis (aPAP) is a rare lung disease caused by the autoantibody against granulocyte-macrophage colony stimulating factor (GM-CSF). The clinical course of aPAP is variable; in severe cases, patients develop lethal respiratory failure due to pulmonary fib...

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Dades bibliogràfiques
Publicat a:BMC Pulm Med
Autors principals: Kinehara, Yuhei, Kida, Hiroshi, Inoue, Yoshikazu, Hirose, Masaki, Nakabayashi, Akihiko, Takeuchi, Yoshiko, Hayama, Yoshitomo, Fukushima, Kiyoharu, Hirata, Haruhiko, Inoue, Koji, Minami, Toshiyuki, Nagatomo, Izumi, Takeda, Yoshito, Funakoshi, Toshiki, Kijima, Takashi, Kumanogoh, Atsushi
Format: Artigo
Idioma:Inglês
Publicat: BioMed Central 2014
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4228074/
https://ncbi.nlm.nih.gov/pubmed/25366193
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/1471-2466-14-172
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