Cargando...

Cholesterol in Niemann–Pick Type C disease

Niemann-Pick Type C (NPC) disease is associated with accumulation of cholesterol and other lipids in late endosomes/lysosomes in virtually every organ; however, neurodegeneration represents the fatal cause for the disease. Genetic analysis has identified loss-of-function mutations in NPC1 and NPC2 g...

Descripción completa

Guardado en:
Detalles Bibliográficos
Autores principales: Bi, Xiaoning, Liao, Guanghong
Formato: Artigo
Lenguaje:Inglês
Publicado: 2010
Materias:
Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4212451/
https://ncbi.nlm.nih.gov/pubmed/20213549
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/978-90-481-8622-8_11
Etiquetas: Agregar Etiqueta
Sin Etiquetas, Sea el primero en etiquetar este registro!