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Left ventricular and aortic dysfunction in cystic fibrosis mice

BACKGROUND: Left ventricular (LV) abnormalities have been reported in cystic fibrosis (CF); however, it remains unclear if loss of cystic fibrosis transmembrane conductance regulator (CFTR) function causes heart defects independent of lung disease. METHODS: Using gut-corrected F508del CFTR mutant mi...

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Main Authors: Sellers, Zachary M., Kovacs, Attila, Weinheimer, Carla J., Best, Philip M.
Formato: Artigo
Idioma:Inglês
Publicado: 2012
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC4170835/
https://ncbi.nlm.nih.gov/pubmed/23269368
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jcf.2012.11.012
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