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Caspase-12 ablation preserves muscle function in the mdx mouse
Duchenne muscular dystrophy (DMD) is a devastating muscle wasting disease caused by mutations in dystrophin. Several downstream consequences of dystrophin deficiency are triggers of endoplasmic reticulum (ER) stress, including loss of calcium homeostasis, hypoxia and oxidative stress. During ER stre...
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| Autors principals: | , |
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| Format: | Artigo |
| Idioma: | Inglês |
| Publicat: |
Oxford University Press
2014
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| Matèries: | |
| Accés en línia: | https://ncbi.nlm.nih.gov/pmc/articles/PMC4168821/ https://ncbi.nlm.nih.gov/pubmed/24879640 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddu249 |
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