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Complement Mutations in Diacylglycerol Kinase-ε–Associated Atypical Hemolytic Uremic Syndrome

BACKGROUND AND OBJECTIVES: Atypical hemolytic uremic syndrome is characterized by vascular endothelial damage caused by complement dysregulation. Consistently, complement inhibition therapies are highly effective in most patients with atypical hemolytic uremic syndrome. Recently, it was shown that a...

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Главные авторы: Sánchez Chinchilla, Daniel, Pinto, Sheila, Hoppe, Bernd, Adragna, Marta, Lopez, Laura, Justa Roldan, Maria Luisa, Peña, Antonia, Lopez Trascasa, Margarita, Sánchez-Corral, Pilar, Rodríguez de Córdoba, Santiago
Формат: Artigo
Язык:Inglês
Опубликовано: American Society of Nephrology 2014
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Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC4152807/
https://ncbi.nlm.nih.gov/pubmed/25135762
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2215/CJN.01640214
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