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Audiologic and Vestibular Findings in Wolfram Syndrome

CONTEXT: Clinical manifestations of Wolfram syndrome (WS), a rare autosomal recessive neurodegenerative disease, include diabetes mellitus (DM), optic nerve atrophy (OA), diabetes insipidus (DI) and sensorineural hearing loss (SNHL). OBJECTIVE: Assessment of auditory and vestibular function in WS pa...

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Autors principals: Karzon, Roanne K., Hullar, Timothy E.
Format: Artigo
Idioma:Inglês
Publicat: 2013
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4142763/
https://ncbi.nlm.nih.gov/pubmed/23698626
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/AUD.0b013e3182944db7
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