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Biophysical Characterisation of Calumenin as a Charged F508del-CFTR Folding Modulator

The cystic fibrosis transmembrane regulator (CFTR) is a cyclic-AMP dependent chloride channel expressed at the apical surface of epithelial cells lining various organs such as the respiratory tract. Defective processing and functioning of this protein caused by mutations in the CFTR gene results in...

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Autori principali: Tripathi, Rashmi, Benz, Nathalie, Culleton, Bridget, Trouvé, Pascal, Férec, Claude
Natura: Artigo
Lingua:Inglês
Pubblicazione: Public Library of Science 2014
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4132023/
https://ncbi.nlm.nih.gov/pubmed/25120007
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0104970
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