Загрузка...
Augmenting ureagenesis in patients with partial carbamyl phosphate synthetase 1deficiency with N-carbamylglutamate
Identical studies employing stable isotopes were performed before and after a 3-day trial of oral N-carbamylglutamate (NCG) in 5 subjects with late onset carbamyl phosphate synthetase deficiency. NCG augmented ureagenesis and decreased plasma ammonia in 4 of 5 subjects. There was marked improvement...
Сохранить в:
| Главные авторы: | , , , , , , |
|---|---|
| Формат: | Artigo |
| Язык: | Inglês |
| Опубликовано: |
2014
|
| Предметы: | |
| Online-ссылка: | https://ncbi.nlm.nih.gov/pmc/articles/PMC4111993/ https://ncbi.nlm.nih.gov/pubmed/24880889 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jpeds.2014.04.012 |
| Метки: |
Добавить метку
Нет меток, Требуется 1-ая метка записи!
|