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N-carbamylglutamate augments ureagenesis and reduces ammonia and glutamine levels in patients with propionic acidemia

OBJECTIVE: To determine whether N-carbamylglutamate reduces plasma levels of ammonia and glutamine and increases ureagenesis rate in patients with propionic acidemia PATIENTS AND METHODS: Identical four-hour studies were performed before and immediately after a 3-day trial of oral N-carbamylglutamat...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Egile Nagusiak: Mew, Nicholas Ah, McCarter, Robert, Daikhin, Yevgeny, Nissim, Itzhak, Yudkoff, Marc, Tuchman, Mendel
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: 2010
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC3297024/
https://ncbi.nlm.nih.gov/pubmed/20566609
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1542/peds.2010-0008
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