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Primary immunodeficiency diagnosed at autopsy: a case report

BACKGROUND: DiGeorge syndrome may manifest as severe immunodeficiency diagnosed at infancy. The diagnosis of primary immunodeficiency is based on characteristic clinical features, immunophenotyping by flow cytometry, molecular diagnostics and functional lymphocyte evaluation. At autopsy, gross evalu...

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Detalhes bibliográficos
Main Authors: Walong, Edwin, Rogena, Emily, Sabai, David
Formato: Artigo
Idioma:Inglês
Publicado em: BioMed Central 2014
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4094674/
https://ncbi.nlm.nih.gov/pubmed/24996427
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/1756-0500-7-425
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