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β–Myosin Heavy Chain Variant Met606Val Causes Very Mild Hypertrophic Cardiomyopathy in Mice, but Exacerbates HCM Phenotypes in Mice Carrying Other HCM Mutations

RATIONALE: ~40% of hypertrophic cardiomyopathy (HCM) is caused by heterozygous missense mutations in β-cardiac myosin heavy chain (βMHC). Associating disease phenotype with mutation is confounded by extensive background genetic and lifestyle/environmental differences between subjects even from the s...

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Autors principals: Blankenburg, Robert, Hackert, Katarzyna, Wurster, Sebastian, Deenen, René, Seidman, J.G., Seidman, Christine E., Lohse, Martin J., Schmitt, Joachim P.
Format: Artigo
Idioma:Inglês
Publicat: 2014
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4086907/
https://ncbi.nlm.nih.gov/pubmed/24829265
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1161/CIRCRESAHA.115.303178
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