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Dysferlin regulates cell membrane repair by facilitating injury-triggered acid sphingomyelinase secretion

Dysferlin deficiency compromises the repair of injured muscle, but the underlying cellular mechanism remains elusive. To study this phenomenon, we have developed mouse and human myoblast models for dysferlinopathy. These dysferlinopathic myoblasts undergo normal differentiation but have a deficit in...

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Détails bibliographiques
Auteurs principaux: Defour, A, Van der Meulen, J H, Bhat, R, Bigot, A, Bashir, R, Nagaraju, K, Jaiswal, J K
Format: Artigo
Langue:Inglês
Publié: Nature Publishing Group 2014
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC4079937/
https://ncbi.nlm.nih.gov/pubmed/24967968
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/cddis.2014.272
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