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No Amelioration of Uromodulin Maturation and Trafficking Defect by Sodium 4-Phenylbutyrate in Vivo: STUDIES IN MOUSE MODELS OF UROMODULIN-ASSOCIATED KIDNEY DISEASE

Uromodulin (UMOD)-associated kidney disease (UAKD) belongs to the hereditary progressive ER storage diseases caused by maturation defects of mutant UMOD protein. Current treatments of UAKD patients are symptomatic and cannot prevent disease progression. Two in vitro studies reported a positive effec...

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Gorde:
Xehetasun bibliografikoak
Egile Nagusiak: Kemter, Elisabeth, Sklenak, Stefanie, Rathkolb, Birgit, Hrabě de Angelis, Martin, Wolf, Eckhard, Aigner, Bernhard, Wanke, Ruediger
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: American Society for Biochemistry and Molecular Biology 2014
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC4036188/
https://ncbi.nlm.nih.gov/pubmed/24567330
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.M113.537035
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