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Lysosomal exocytosis and lipid storage disorders

Lysosomes are acidic compartments in mammalian cells that are primarily responsible for the breakdown of endocytic and autophagic substrates such as membranes, proteins, and lipids into their basic building blocks. Lysosomal storage diseases (LSDs) are a group of metabolic disorders caused by geneti...

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Autors principals: Samie, Mohammad Ali, Xu, Haoxing
Format: Artigo
Idioma:Inglês
Publicat: The American Society for Biochemistry and Molecular Biology 2014
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4031951/
https://ncbi.nlm.nih.gov/pubmed/24668941
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1194/jlr.R046896
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