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Biology and Genetics of Prions Causing Neurodegeneration

Prions are proteins that acquire alternative conformations that become self-propagating. Transformation of proteins into prions is generally accompanied by an increase in β-sheet structure and a propensity to aggregate into oligomers. Some prions are beneficial and perform cellular functions, wherea...

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Autore principale: Prusiner, Stanley B.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2013
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4010318/
https://ncbi.nlm.nih.gov/pubmed/24274755
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1146/annurev-genet-110711-155524
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