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Incontinentia pigmenti
Incontinentia pigmenti is a rare genodermatosis in which the skin involvement occurs in all patients. Additionally, other ectodermal tissues may be affected, such as the central nervous system, eyes, hair, nails and teeth. The disease has a X-linked dominant inheritance pattern and is usually lethal...
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| Autors principals: | , , , , , , , , , , , , |
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| Format: | Artigo |
| Idioma: | Inglês |
| Publicat: |
Sociedade Brasileira de Dermatologia
2014
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| Matèries: | |
| Accés en línia: | https://ncbi.nlm.nih.gov/pmc/articles/PMC3938351/ https://ncbi.nlm.nih.gov/pubmed/24626645 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1590/abd1806-4841.20142584 |
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