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Incontinentia pigmenti

Incontinentia pigmenti is a rare genodermatosis in which the skin involvement occurs in all patients. Additionally, other ectodermal tissues may be affected, such as the central nervous system, eyes, hair, nails and teeth. The disease has a X-linked dominant inheritance pattern and is usually lethal...

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Sonraí Bibleagrafaíochta
Main Authors: Poziomczyk, Cláudia Schermann, Recuero, Júlia Kanaan, Bringhenti, Luana, Santa Maria, Fernanda Diffini, Campos, Carolina Wiltgen, Travi, Giovanni Marcos, Freitas, André Moraes, Maahs, Marcia Angelica Peter, Zen, Paulo Ricardo Gazzola, Fiegenbaum, Marilu, de Almeida, Sheila Tamanini, Bonamigo, Renan Rangel, Bau, Ana Elisa Kiszewski
Formáid: Artigo
Teanga:Inglês
Foilsithe: Sociedade Brasileira de Dermatologia 2014
Ábhair:
Rochtain Ar Líne:https://ncbi.nlm.nih.gov/pmc/articles/PMC3938351/
https://ncbi.nlm.nih.gov/pubmed/24626645
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1590/abd1806-4841.20142584
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