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Accumulation of coated vesicles bearing mannose 6-phosphate receptors for lysosomal enzymes in the Golgi region of I-cell fibroblasts.

The distribution of mannose 6-phosphate (Man6P) receptors for lysosomal enzymes was investigated in human normal and mucolipidosis II (I-cell) disease fibroblasts by light and electron microscopic immunocytochemistry. In normal fibroblasts whose lysosomal enzymes contain Man6P recognition markers re...

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Autors principals: Brown, W J, Farquhar, M G
Format: Artigo
Idioma:Inglês
Publicat: 1984
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC391652/
https://ncbi.nlm.nih.gov/pubmed/6147848
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