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Molecular heterogeneity of variant isovaleryl-CoA dehydrogenase from cultured isovaleric acidemia fibroblasts.

Variants of isovaleryl-CoA dehydrogenase (IVDHase, EC 1.3.99.10) in 15 isovaleric acidemia fibroblast lines were analyzed using [35S]methionine labeling, immunoprecipitation with anti-rat IVDHase antiserum, and NaDodSo4/polyacrylamide gel electrophoresis. Five distinct variants of IVDHase were detec...

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Dades bibliogràfiques
Publicat a:Proc Natl Acad Sci U S A
Autors principals: Ikeda, Y, Keese, S M, Tanaka, K
Format: Artigo
Idioma:Inglês
Publicat: National Academy of Sciences 1985
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Accés en línia:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC391314/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/3863140/
https://ncbi.nlm.nih.govhttps://doi.org/10.1073/pnas.82.20.7081
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