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Molecular heterogeneity of variant isovaleryl-CoA dehydrogenase from cultured isovaleric acidemia fibroblasts.

Variants of isovaleryl-CoA dehydrogenase (IVDHase, EC 1.3.99.10) in 15 isovaleric acidemia fibroblast lines were analyzed using [35S]methionine labeling, immunoprecipitation with anti-rat IVDHase antiserum, and NaDodSo4/polyacrylamide gel electrophoresis. Five distinct variants of IVDHase were detec...

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Bibliografski detalji
Glavni autori: Ikeda, Y, Keese, S M, Tanaka, K
Format: Artigo
Jezik:Inglês
Izdano: 1985
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC391314/
https://ncbi.nlm.nih.gov/pubmed/3863140
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