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Decreasing Levels of the cdk5 Activators, p25 and p35, Reduces Excitotoxicity in Striatal Neurons

Huntington’s disease (HD) is a progressive neurodegenerative disorder caused by an expanded CAG trinucleotide repeat sequence in the huntingtin gene. The resulting poly-glutamine expansion in the huntingtin protein imparts a novel toxic gain of function causing selective loss of medium spiny neurons...

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Autori principali: Park, Kevin H.J., Lu, Ge, Fan, Jing, Raymond, Lynn A., Leavitt, Blair R.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2012
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3864911/
https://ncbi.nlm.nih.gov/pubmed/24353748
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3233/JHD-2012-129000
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