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A Case of Congenital Erythropoietic Porphyria without Hemolysis

Porphyrias are group of disorders caused by deficiency of the enzymes in heme synthetic pathway. Congenital erythropoietic porphyria (CEP) is an extremely rare disease with mutation in the gene that codes for uroporphyrinogen III synthase leading to accumulation of porphyrin in different tissues and...

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Autori principali: De, Arun K, Das, Kallol, Sil, Archan, Joardar, Swarnali
Natura: Artigo
Lingua:Inglês
Pubblicazione: Medknow Publications & Media Pvt Ltd 2013
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3778801/
https://ncbi.nlm.nih.gov/pubmed/24082206
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/0019-5154.117336
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