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The emerin-binding transcription factor Lmo7 is regulated by association with p130Cas at focal adhesions

Loss of function mutations in the nuclear inner membrane protein, emerin, cause X-linked Emery-Dreifuss muscular dystrophy (X-EDMD). X-EDMD is characterized by contractures of major tendons, skeletal muscle weakening and wasting, and cardiac conduction system defects. The transcription factor Lmo7 r...

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Autors principals: Wozniak, Michele A., Baker, Brendon M., Chen, Christopher S., Wilson, Katherine L.
Format: Artigo
Idioma:Inglês
Publicat: PeerJ Inc. 2013
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3757464/
https://ncbi.nlm.nih.gov/pubmed/24010014
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.7717/peerj.134
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