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Serum heat shock protein 47 levels are elevated in acute exacerbation of idiopathic pulmonary fibrosis

Little is known about the pathophysiology of acute exacerbation (AE) of idiopathic pulmonary fibrosis (IPF). Heat shock protein 47 (HSP47), a collagen-specific molecular chaperone, is essential for biosynthesis and secretion of collagen molecules. Previous studies in experimental animal fibrosis mod...

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Autors principals: Kakugawa, Tomoyuki, Yokota, Shin-ichi, Ishimatsu, Yuji, Hayashi, Tomayoshi, Nakashima, Shota, Hara, Shintaro, Sakamoto, Noriho, Kubota, Hiroshi, Mine, Mariko, Matsuoka, Yasuhiro, Mukae, Hiroshi, Nagata, Kazuhiro, Kohno, Shigeru
Format: Artigo
Idioma:Inglês
Publicat: Springer Netherlands 2013
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3745258/
https://ncbi.nlm.nih.gov/pubmed/23435730
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s12192-013-0411-5
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