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RACK1 interacts with filamin-A to regulate plasma membrane levels of the cystic fibrosis transmembrane conductance regulator

Mutations in cystic fibrosis transmembrane regulator (CFTR), a chloride channel in the apical membranes of secretory epithelial cells, underlie the fatal genetic disorder cystic fibrosis. Certain CFTR mutations, including the common mutation ΔF508-CFTR, result in greatly decreased levels of active C...

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Autori principali: Smith, Laura, Litman, Paul, Kohli, Ekta, Amick, Joseph, Page, Richard C., Misra, Saurav, Liedtke, Carole M.
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Physiological Society 2013
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3725521/
https://ncbi.nlm.nih.gov/pubmed/23636454
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1152/ajpcell.00026.2013
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