Enhancement of Residual Arylsulfatase B Activity in Feline Mucopolysaccharidosis VI by Thiol-induced Subunit Association

The molecular pathology of the deficient arylsulfatase B activity in feline mucopolysaccharidosis (MPS) VI was investigated. Compared with the highly purified normal feline hepatic enzyme, the purified MPS VI residual activity had a 100-fold higher Michaelis constant (K(m)), an altered electrophoret...

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Detalles Bibliográficos

Publicado en:	J Clin Invest
Autores principales:	Vine, Deborah T., McGovern, Margaret M., Schuchman, Edward H., Haskins, Mark E., Desnick, Robert J.
Formato:	Artigo
Lenguaje:	Inglês
Publicado:	American Society for Clinical Investigation 1982
Materias:	Articles
Acceso en línea:	https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC370978/ https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/6799547/ https://ncbi.nlm.nih.govhttps://doi.org/10.1172/JCI110452
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