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Adenosine deaminase messenger RNAs in lymphoblast cell lines derived from leukemic patients and patients with hereditary adenosine deaminase deficiency.

Hereditary deficiency of adenosine deaminase (ADA) usually causes profound lymphopenia with severe combined immunodeficiency disease. Cells from patients with ADA deficiency contain less than normal, and sometimes undetectable, amounts of ADA catalytic activity and ADA protein. The molecular defects...

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Detalles Bibliográficos
Autores principales: Adrian, G S, Hutton, J J
Formato: Artigo
Lenguaje:Inglês
Publicado: 1983
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC370370/
https://ncbi.nlm.nih.gov/pubmed/6134754
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