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Inherited disorders of GABA metabolism

The inherited disorders of γ-amino butyric acid (GABA) metabolism require an increased index of clinical suspicion. The known genetic disorders are GABA-transaminase deficiency, succinic semialdehyde dehydrogenase (SSADH) deficiency and homocarnosinosis. A recent link has also been made between impa...

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Bibliografiske detaljer
Main Authors: Pearl, Phillip L, Hartka, Thomas R, Cabalza, Jessica L, Taylor, Jacob, Gibson, Michael K
Format: Artigo
Sprog:Inglês
Udgivet: 2006
Fag:
Online adgang:https://ncbi.nlm.nih.gov/pmc/articles/PMC3675887/
https://ncbi.nlm.nih.gov/pubmed/23842532
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2217/14796708.1.5.631
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