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Structural, Compositional, and Biomechanical Alterations of the Lumbar Spine in Rats with Mucopolysaccharidosis Type VI (Maroteaux–Lamy Syndrome)

Mucopolysaccharidosis (MPS) VI is an inherited lysosomal storage disorder resulting from deficiency of N-acetylgalactosamine-4-sulfatase activity and subsequent accumulation of incompletely degraded dermatan sulfate (DS) containing glycosaminoglycans (GAGs). Painful spinal deformities are commonly f...

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Autors principals: Lai, Alon, Simonaro, Calogera M., Schuchman, Edward H., Ge, Yi, Laudier, Damien M., Iatridis, James C.
Format: Artigo
Idioma:Inglês
Publicat: 2012
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3645935/
https://ncbi.nlm.nih.gov/pubmed/23192728
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/jor.22281
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