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Regulation of Torsin ATPases by LAP1 and LULL1
TorsinA is a membrane-associated AAA+ (ATPases associated with a variety of cellular activities) ATPase implicated in primary dystonia, an autosomal-dominant movement disorder. We reconstituted TorsinA and its cofactors in vitro and show that TorsinA does not display ATPase activity in isolation; AT...
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| Main Authors: | , , , , |
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| Format: | Artigo |
| Sprog: | Inglês |
| Udgivet: |
National Academy of Sciences
2013
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| Fag: | |
| Online adgang: | https://ncbi.nlm.nih.gov/pmc/articles/PMC3637692/ https://ncbi.nlm.nih.gov/pubmed/23569223 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1300676110 |
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