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Melanocytes—A Novel Tool to Study Mitochondrial Dysfunction in Duchenne Muscular Dystrophy

Dystrophin is a subsarcolemmal protein that, by linking the actin cytoskeleton to the extracellular matrix via dystroglycans, is critical for the integrity of muscle fibers. Here, we report that epidermal melanocytes, obtained from conventional skin biopsy, express dystrophin with a restricted local...

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Main Authors: Pellegrini, Camilla, Zulian, Alessandra, Gualandi, Francesca, Manzati, Elisa, Merlini, Luciano, Michelini, Maria E, Benassi, Luisa, Marmiroli, Sandra, Ferlini, Alessandra, Sabatelli, Patrizia, Bernardi, Paolo, Maraldi, Nadir M
Format: Artigo
Jezik:Inglês
Izdano: Wiley Subscription Services, Inc., A Wiley Company 2013
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC3601437/
https://ncbi.nlm.nih.gov/pubmed/23169061
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/jcp.24290
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