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Leukocyte Adhesion Deficiency-I variant Syndrome (LAD-Iv, LAD-III): Molecular Characterization of the Defect in an Index Family

Leukocyte adhesion deficiencies are rare clinical syndromes of impaired host defense that provide novel insights into regulation of immune and inflammatory responses (1,2). Leukocyte adhesion deficiency (LAD)-I variant (LAD-Iv), also called LAD-III, is a unique disorder in which inside-out signaling...

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Detalhes bibliográficos
Main Authors: Harris, ES, Smith, TL, Springett, GM, Weyrich, AS, Zimmerman, GA
Formato: Artigo
Idioma:Inglês
Publicado em: 2011
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3564639/
https://ncbi.nlm.nih.gov/pubmed/22139635
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/ajh.22253
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