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Sod1 Deficiency Reduces Incubation Time in Mouse Models of Prion Disease

Prion infections, causing neurodegenerative conditions such as Creutzfeldt-Jakob disease and kuru in humans, scrapie in sheep and BSE in cattle are characterised by prolonged and variable incubation periods that are faithfully reproduced in mouse models. Incubation time is partly determined by genet...

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Dettagli Bibliografici
Autori principali: Akhtar, Shaheen, Grizenkova, Julia, Wenborn, Adam, Hummerich, Holger, Fernandez de Marco, Mar, Brandner, Sebastian, Collinge, John, Lloyd, Sarah E.
Natura: Artigo
Lingua:Inglês
Pubblicazione: Public Library of Science 2013
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3551847/
https://ncbi.nlm.nih.gov/pubmed/23349894
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0054454
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