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Advance in the pathogenesis and treatment of Wilson disease

Wilson disease is an autosomal recessive disorder of copper metabolism. Diagnosis depends primarily on clinical features, biochemical parameters and the presence of the Kayser-Fleischer ring. Genetic analysis for mutations within ATP7B is a convincing diagnostic tool. The traditional treatment for W...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Egile Nagusiak: Dong, Qin-Yun, Wu, Zhi-Ying
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: BioMed Central 2012
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC3526418/
https://ncbi.nlm.nih.gov/pubmed/23210912
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/2047-9158-1-23
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