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Advance in the pathogenesis and treatment of Wilson disease

Wilson disease is an autosomal recessive disorder of copper metabolism. Diagnosis depends primarily on clinical features, biochemical parameters and the presence of the Kayser-Fleischer ring. Genetic analysis for mutations within ATP7B is a convincing diagnostic tool. The traditional treatment for W...

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Autori principali: Dong, Qin-Yun, Wu, Zhi-Ying
Natura: Artigo
Lingua:Inglês
Pubblicazione: BioMed Central 2012
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3526418/
https://ncbi.nlm.nih.gov/pubmed/23210912
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/2047-9158-1-23
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