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Fibrodysplasia ossificans progressiva: mechanisms and models of skeletal metamorphosis
Fibrodysplasia ossificans progressiva (FOP; MIM #135100) is a debilitating genetic disorder of connective tissue metamorphosis. It is characterized by malformation of the great (big) toes during embryonic skeletal development and by progressive heterotopic endochondral ossification (HEO) postnatally...
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| Autors principals: | , , |
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| Format: | Artigo |
| Idioma: | Inglês |
| Publicat: |
The Company of Biologists Limited
2012
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| Matèries: | |
| Accés en línia: | https://ncbi.nlm.nih.gov/pmc/articles/PMC3484858/ https://ncbi.nlm.nih.gov/pubmed/23115204 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1242/dmm.010280 |
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