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A preliminary score for the assessment of disease activity in hereditary recurrent fevers: results from the AIDAI (Auto-Inflammatory Diseases Activity Index) Consensus Conference

BACKGROUND: The systemic autoinflammatory disorders (SAID) share many clinical manifestations, albeit with variable patterns, intensity and frequency. A common definition of disease activity would be rational and useful in the management of these lifelong diseases. Moreover, standardised disease act...

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Autores principales: Piram, Maryam, Frenkel, Joost, Gattorno, Marco, Ozen, Seza, Lachmann, Helen J, Goldbach-Mansky, Raphaela, Hentgen, Véronique, Neven, Bénédicte, Stankovic Stojanovic, Katia, Simon, Anna, Kuemmerle-Deschner, Jasmin, Hoffman, Hal, Stojanov, Silvia, Duquesne, Agnès, Pillet, Pascal, Martini, Alberto, Pouchot, Jacques, Koné-Paut, Isabelle
Formato: Artigo
Lenguaje:Inglês
Publicado: 2010
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3463866/
https://ncbi.nlm.nih.gov/pubmed/21081528
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/ard.2010.132613
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