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Lamin A/C Mutants Disturb Sumo1 Localization and Sumoylation in Vitro and in Vivo

A-type lamins A and C are nuclear intermediate filament proteins in which mutations have been implicated in multiple disease phenotypes commonly known as laminopathies. A few studies have implicated sumoylation in the regulation of A-type lamins. Sumoylation is a post-translational protein modificat...

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Detalhes bibliográficos
Main Authors: Boudreau, Émilie, Labib, Sarah, Bertrand, Anne T., Decostre, Valérie, Bolongo, Pierrette M., Sylvius, Nicolas, Bonne, Gisèle, Tesson, Frédérique
Formato: Artigo
Idioma:Inglês
Publicado em: Public Library of Science 2012
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3448699/
https://ncbi.nlm.nih.gov/pubmed/23029315
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0045918
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