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TLR-Mediated B Cell Defects and IFN-α in Common Variable Immunodeficiency

Common variable immune deficiency (CVID) B cells have impaired responses to TLR7 and TLR9 agonists including poor cell proliferation, loss of cytokine production, and failure to produce IgG or IgA. We show that TLR7- or 9-activated B cells from CVID subjects with >0.5% peripheral isotype-switched...

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Autori principali: Yu, Joyce E., Zhang, Li, Radigan, Lin, Sanchez-Ramon, Silvia, Cunningham-Rundles, Charlotte
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2011
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3428015/
https://ncbi.nlm.nih.gov/pubmed/22048980
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s10875-011-9602-y
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