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Oculodentodigital Syndrome with Syndactyly Type III in a Pakistani consanguineous family

BACKGROUND: Oculodentodigital syndrome (ODD; OMIM #164200) is a rare autosomal dominant disorder with pleiotropic effects. It is caused by mutation in gap junction protein α 1 (GJA1) gene which encodes connexion 43. ODD is characterised by symptoms i.e. craniofacial, neurologic, limb, ocular abnorma...

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Bibliografiske detaljer
Main Authors: Nishat, Sumaira, Mansoor, Qaisar, Javaid, Amara, Ismail, Muhammad
Format: Artigo
Sprog:Inglês
Udgivet: Specjalisci Dermatolodzy 2012
Fag:
Online adgang:https://ncbi.nlm.nih.gov/pmc/articles/PMC3399675/
https://ncbi.nlm.nih.gov/pubmed/22826718
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3315/jdcr.2012.1094
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